An infant with congenital midaortic syndrome

Hacer YAPICIOĞLU YILDIZDAŞ; Sevcan ERDEM; Fadli DEMİR; Hüseyin ŞİMŞEK; Ferda ÖZLÜ

doi:https://doi.org/10.17826/cumj.335980

Article Details

An infant with congenital midaortic syndrome

Authors:

Hacer YAPICIOĞLU YILDIZDAŞ | Sevcan ERDEM | Fadli DEMİR | Hüseyin ŞİMŞEK | Ferda ÖZLÜ

Publisher:

Cukurova University

Main Topics:

Promotion of health

Journal:

Cukurova Medical Journal 2018 Vol.43 Issue 4, pp.1042-1044

Document Type:

Article

Publication Date:

12/2018

Document Language:

English

Document ID (Org No.):

2000915992

Frequency:

Quarterly

eISSN:

2602-3040

pISSN:

2602-3032

DOI:

https://doi.org/10.17826/cumj.335980

Keywords:

Abstract:

 


Midaortic syndrome is an uncommon disease characterized by segmental or diffuse narrowing of abdominal or distal descending thorasic aorta. Majority of the cases are idiopathic but some are secondary to fibromuscular dysplasia, giant cell arteritis, Moyamoya disease or genetic diseases such as neurofibromatosis, Williams’ syndrome and Alagille syndrome. It is very rare in newborn period.  Here we present a 40 days old infant who admitted to hospital for respiratory distress, hypertension, heart failure and was diagnosed as midaortic syndrome. She had medical treatment but unfortunately died due to heart failure when she was two months old age.

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Midaortik sendrom nadir bir hastalık olup abdominal veya distal inen aortanın segmental veya difüz darlığı ile karakterizedir. Olguların çoğu idiyopatik olmakla birlikte bir kısmı da fibromüsküler displazi, dev hücreli aterit, Moyamoya hastalığı veya nörofibramatozis, Williams’ sendromu ve Alagille sendromu gibi genetik hastalıklara ikincildir. Burada 40 günlük iken hastaneye solunum sıkıntısı, kalp yetmezliği tablosunda başvuran ve midaortik sendrom tanısı alan bir olgu sunulmuştur. Olguda medikal tedavi tercih edilmiş ancak bebek iki aylık iken eksitus olmuştur. 





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Article Details

An infant with congenital midaortic syndrome

Authors:

Hacer YAPICIOĞLU YILDIZDAŞ | Sevcan ERDEM | Fadli DEMİR | Hüseyin ŞİMŞEK | Ferda ÖZLÜ

Publisher:

Cukurova University

Main Topics:

Promotion of health

Journal:

Cukurova Medical Journal 2018 Vol.43 Issue 4, pp.1042-1044

Document Type:

Article

Publication Date:

12/2018

Document Language:

English

Document ID (Org No.):

2000915992

Frequency:

Quarterly

eISSN:

2602-3040

pISSN:

2602-3032

DOI:

https://doi.org/10.17826/cumj.335980

Midaortik sendrom

aort koartasyonu

Issues

Article Details

An infant with congenital midaortic syndrome

Authors: Hacer YAPICIOĞLU YILDIZDAŞ | Sevcan ERDEM | Fadli DEMİR | Hüseyin ŞİMŞEK | Ferda ÖZLÜ

Publisher: Cukurova University

Main Topics: Promotion of health

Journal: Cukurova Medical Journal 2018 Vol.43 Issue 4, pp.1042-1044

Document Type: Article

Publication Date: 12/2018

Document Language: English

Document ID (Org No.): 2000915992

Frequency: Quarterly

eISSN: 2602-3040

pISSN: 2602-3032

DOI: https://doi.org/10.17826/cumj.335980

Midaortik sendrom

aort koartasyonu

Issues

Authors:

Hacer YAPICIOĞLU YILDIZDAŞ | Sevcan ERDEM | Fadli DEMİR | Hüseyin ŞİMŞEK | Ferda ÖZLÜ

Publisher:

Cukurova University

Main Topics:

Promotion of health

Journal:

Cukurova Medical Journal 2018 Vol.43 Issue 4, pp.1042-1044

Document Type:

Article

Publication Date:

12/2018

Document Language:

English

Document ID (Org No.):

2000915992

Frequency:

Quarterly

eISSN:

2602-3040

pISSN:

2602-3032

DOI:

https://doi.org/10.17826/cumj.335980